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ۼ : 22-03-17 14:08
1 б ǰ Űб1 , б
 ۾ :
ȸ : 1,883  

ߴ(primary metabolic myopathy) õ 
μ 1951 McArdle ó 
Ǿ. (glycogen storage
myopathy), (lipid storage myoapthy), 
縳ü(mitochondrial myopathy), ̿ƵҷƮŻ
ƹ̳ȿ (myoadenylate deaminase deficiency)
еǸ, ̻ , ټ࿡ ʿ
Ͽ ߻Ѵ. 
ռ(glycogen synthesis), (glycogenolysis)
Ȥ شۿ(glycolysis) õ ں
߻ϴ ȯ, I XI
, , ѷ I(Von 
Gierkes disease) VI
õ 缺 ˷. ڵ ֱ
1 Ͽ⿡ ϴ
̴.

 
 

Total 22
ȣ     ۾ ¥ ȸ
MIT ȣ( Ventilator) 07-29 1870
22 Ҿ ܰ ġ б ǰ Ҿưб 03-17 1047
21 1 б ǰ Űб1 03-17 1884
20 ̿ñ ȯڿ Dysferlin (4) 03-17 1403
19 MIT ȣ( Ventilator) 07-29 1870
18 䳢 ô ջ Ұ ȿ (2) 04-11 4217
17 Ұ 踦 Դϴ. (2) 04-11 4661
16 Inhalation of hydrogen gas attenuates cisplatin-induced otot 10-14 3873
15 Ұ Դϴ. (1) 09-20 5493
14 Ұ ڷԴϴ. (1) 09-20 7356
13 ǰ Ͽ-4 03-13 4141
12 ǰ Ͽ-3 03-12 4500
11 ǰ Ͽ-2 03-12 3770
10 ǰ Ͽ, 03-12 3411
9 渶 ´ ִ 09-04 3483
8 ȿ(ó: ǿ) 09-04 4460
7 (ó- ǿ) 09-04 3724
6 ׻ȭ ǰ, Ȱ ſ 09-04 4794
5 ҿ 09-04 3707
4 ϴ 09-04 9727
3 Ұ ޵Ǹ ̷ п Ư ϴ. (1) 09-04 3456
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